Case 2/2015 A 33-Year-Old Woman with Double Right Ventricular Chamber and Ventricular Septal Defect

Echocardiogram (Figure 2) showed right ventricular inflow tract stenosis causing an intraventricular gradient of 80 mmHg, with a 13-mm diameter ventricular septal defect partially occluded by the tricuspid valve, thus resulting in an effective 4.7-mm orifice. There was RV hypertrophy with mildly enlarged right cardiac chambers. Gradient between ventricles was 82 mmHg. There was a small aneurysm formation in the ventricular septum. Measurements were as follows: left ventricle (LV) = 45 mm; left atrium (LA) = 32; Ao = 26; septum = posterior wall = 7 mm. LV ejection fraction = 66%. There was a 3-mm foramen ovale with bidirectional predominantly left-to-right shunt. RV systolic pressure = 110 mmHg.